Isolated Right Sided Anomalous Pulmonary Venous Connection Associated with Significant Right Ventricular Enlargement and Intact Interatrial Septum

Partial anomalous pulmonary venous connection (PAPVC) is a very rare congenital heart disease where one or more of the pulmonary veins are connected to the venous circulation. Although initially suspected with inexplicable right ventricular enlargement on transthoracic echocardiography, other modalities such as transesophageal echocardiography, CT angiography or cardiac Magnetic resonance (CMR) imaging are able to diagnosis the anatomical abnormalities. We present a 29-year-old female with moderate right ventricular enlargement and isolated right upper and middle pulmonary vein anomalous return to superior vena cava.