Report of Ephithelioid Sarcoma Occurance in a Patient with Inguinal Hernia Manifestation

Epithelioid sarcoma is one of the malignant soft tissue tumors of uncertain type has been applied to a morphologically distinctive neoplasm which characteristically affects the distal parts of the extremities of young adults. In fact epithelioid sarcoma is the most common soft tissue sarcoma in the hand and wrist. This article is a case report of the tumor followed by operation of inguinal hernia in 32 years old male. At first with uncommon manifestation and site of tumor another differential diagnosis was suggested such as abscess, GI malignacies. In supplementary evaluation and biopsy of ulcer the diagnosis focused on undifferentiated high grade epithelial tumor highly suggestive Epithelioid sarcoma. In Immunohisochemical finding, CD34 and, cytokeratin, this diagnosis was confirmed. The most important point was the role of surgical trauma in disease flare up. The best strategy in management of Ephithelioid Sarcoma is extensive resection amputation for relative long survival.