Cardiac Arrest in a Case of Mucopolysaccharidosis after Tracheostomy

Airway management during induction of anesthesia is difficult in some metabolic disorders like mucopolysaccharidosis (MPS). In this article we report an 11 years old child with Hurler-Scheie syndrome how was admitted to operating room for thracheostomy under general anesthesia. Mask ventilation was difficult and endotracheal intubation was impossible and anesthesiologist ventilated the patients lung by inserting laryngeal mask airway. The purpose of this article is to increase awareness among anesthetists and surgeons about the anatomical and pathophysiological changes in these syndrome which may lead to severe airway problems and complications in perioperative period.