Marcus Gunn jaw winking syndrome; a case with only severe retraction

Marcus Gunn jaw winking syndrome (MGJWS) first described in 1883 by Marcus Gunn is a synkinesis of masticatory muscles (usually) and levator palpebrae superioris resulting in a synchronic eyelid and pterygoid muscles contraction. It is a rare, congenital, unilateral and non-progressive eye synkinesis usually first noticed by mother feeding or nursing the baby. Although association of systemic anomalies with MGJWS are rare but ocular associations are common and with their average prevalence include: anisometropia (15%), amblyopia (45%) and strabismus (55%) that most of them should be managed as soon as possible for preventing vision loss. Before any surgical repair, medical treatment should be considered for possible ocular associations. The most disturbing aspect of the jaw-winking syndrome maybe rapid, abnormal and involuntary motion of the eyelid. We report a case with MGJWS without any ptosis just presenting with eyelid retraction and special social and behavioral aspects making the patient not to face any public environment and always worried about his appearance as seen by others.