فهرست مطالب فرید چکنی

Neuroacanthocytosis, a rare neurodegenerative disorder, is commonly transmitted in autosomal recessive pattern. It accompanies with several movement abnormalities such as tics, orofacial dystonia, tongue and lip biting, and absent tendon reflexes. Behavioral and cognitive changes occur frequently. Acanthocytosis with normal serum lipoproteins is a characteristic finding in this syndrome. A case of neuroacanthocytosis is presented in this article.Case report: The patient was a 37 years old man, referred to Neurology Department for progressive weakness, behavioral changes, chorea, vocal tics, orofacial dystonia, cough and fever. The diagnosis was proved by several assessments. He was treated for the complication of aspiration pneumonia and his movement disorder and recovered relatively. Although rare, this condition is present in our country thus it should be considered for all patients with movement and cognitive disorders.

ntroduction: Petrositis, osteomyelitis of temporal bone, is a rare complication of middle ear infection or mastoiditis. Symptoms reported in patients with petrositis are otalgia, deep facial pain, headache, otorrhea, fever, coma and cranial nerve paralysis. Current diagnostic tests for this complication include high-resolution CT scan, brain MRI and bone scan with Technetium, Gallium and Indium 1-11.Case report: A 34 years old lady with left multiple cranial nerves palsies of VII, VIII, IX, X, XII is presented. She had a history of otitis media and then mastoiditis in left side 6 months ago which was underwent tympanomastoidectomy. In radiological studies there was involvement of parameninge tissue next to petrous bone. Gallium scan was highly suggestive for petrous osteomyelitis. She was treated with empiric parenteral antibiotics and her symptoms resolved completely.