Teratoid wilms tumor: Case Report and Review of Literature

Teratoid Wilm’s tumor (TWT) is a rare variant of Wilm’s tumor composed of well-differentiated epithelial and/or mesenchymal heterologous elements constituting more than 50% of the conventional wilm’s tumor. The teratoid histologic variant of Wilms’ tumor is rare, with only 33 prior reported cases of Renal Teratoid Wilms tumor and 5 cases of extra renal Teratoid wilms tumor.  We have summarized the characteristics of these cases. Among the 33 reported cases, the age ranged from 3 month to 7 years, locations of tumors in these reports are limited to renal region. Histology varied from predominant mesenchymal component to heterologous epithelial components and a mixed pattern. A Teratoid Wilms’ tumors hence appears to present at a high stage. Treatment strategies should focus on wide total surgical resection due to this entity’s poor response to chemotherapy. We hereby report an additional case in a 6 year old female along with review of literature.