A pigmented calcifying cystic odontogenic tumor associated with odontoma: A case report

Introdution: Pigmented intraosseous odontogenic lesions are rare, with only 47 reported cases in the English literature. Among them, pigmented calcifying cystic odontogenic tumor, formerly known as calcifying odontogenic cyst, is the most common lesion with 20 reported cases.Case Report: The patient was a 19-year-old man. He had a bony, tender expansion in anterior right maxillary region extended to orbital rim with visual complaints and unilateral headache. Considering radiographic appearance, microscopic study, special and immunohistochemical staining, a diagnosis of pigmented calcifiying cystic odontogenic tumor associated with odontoma was rendered. Due to the same neural crest origin for melanocytes and dental lamina, the presence of melanocytes and melanin in this lesion is accountable. However, till now, no biologic behavioral and prognostic role has been considered for it. This case will add to rare reported cases of pigmented odontogenic lesions.